Spontaneous ruptured choledochal cyst in a child presenting with bilious ascites: A case report
Keywords:
choledochal cyst, bilious ascites, ascitesAbstract
Background: Choledochal cyst is a rare congenital abnormal dilatation of the biliary tract, with the potential for premalignancy. Clinical presentations depend on the size of cyst and the age of onset. Only 2% show a triad of abdominal pain, abdominal mass and cholestasis jaundice. This pediatric case is an unusual presentation with bilious peritonitis.
Case presentation: We are reporting a 2-year-old girl, first diagnosed with choledochal cyst. She presented with progressive abdominal discomfort and abdominal distension for 13 days. Abdominal peracentesis revealed bilious ascites with infection. An exporatory laporatomy revealed gangrenous choledochal cyst with rupture. Cystectomy with Rouen-Y hepaticojejunmostomy were performed. Her clinical conditon improve after surgery.
Conclusion: The 2-year-old girl, newly diagnosed with choledochal cyst presented with bilious ascites, without previous history of jaundice, which is a rare presentation.
Downloads
References
Holcomb GW, Murphy JP. Holocomb and Ashcraft’s pediatric Surgery. In: Liem NT, Benedict LA, Holocomb GW. Choledochal cyst and Gallbladder disease. 7th ed. London: ELSEVIER, 2020:695-708.
Tsai CC, Huang PK, Liu HK, Su YT, Yang MC, Yeh ML. Pediatric types I and VI choledochal cysts complicated with acute pancreatitis and spontaneous perforation: A case report and literature review. Medicine (Baltimore). 2017;96(42):e8306.
Treem WR, Hyams JS, McGowan GS, Sziklas J. Spontaneous rupture of a choledochal cyst: clues to diagnosis and etiology. J Pediatr Gastroenterol Nutr. 1991;13(3):301–6.
Song HK, Kim MH, Myung SJ, Lee SK, Kim HJ, Yoo KS, et al. Choledochal cyst associated the with anomalous union of pancreaticobiliary duct (AUPBD) has a more grave clinical course than choledochal cyst alone. Korean J Intern Med. 1999;14(2):1–8.
Chayutra Intrakamhaeng. Choledochal cyst.; [Cited 8 December 2022] Available from: http://www.pedsurgery.md.chula.ac.th/Choledochal cyst.
Harper L, Lavrand F, Pietrera P, Loot M, Vergnes P. Spontaneous rupture of a choledochal cyst in a 11-month-old girl. Arch Pediatr. 2006;13(2):156–8.
Han SJ, Hwang EH, Chung KS, Kim MJ, Kim H. Acquired choledochal cyst from anomalous pancreatobiliary duct union. J Pediatr Surg. 1997;32(12):1735–8.
Gupta A, Chakaravarthi K, Kaman L. Spontaneous rupture of a choledochal cyst during post partum: A rare presentation. Gastroenterology Res. 2017 Apr;10(2):128–31.
Chongsrisawat V, Roekwibunsi S, Mahayosnond A, Kingpetch K, Poovorawan Y. Spontaneous choledochal cyst rupture in a child. Pediatr Surg Int. 2004;20(10):811–2.
Downloads
Published
How to Cite
Issue
Section
License
Copyright (c) 2024 The Royal College of Pediatricians Of Thailand

This work is licensed under a Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License.